Stiff Person sendromlu hastanın Gordon’un fonksiyonel sağlık örüntüleri modeli doğrultusunda öz etkililik-yeterlilik durumunun incelenmesi-olgu sunumu
Abstract
Stiff Person Sendromu, kaslarda rijidite, ani myoklonik sıçrama ve spazmlar ile tonik aktiviteler şeklinde seyreden otoimmün bir hastalıktır. Hasta A.K.’nin şikayetleri sol kolda kasılma şeklinde ortaya çıkmış daha sonra sağ kol ve sırt bölgesine yayılmıştır. Kasılmalar ve hareket etmekle şiddeti artan ağrılardan rahatsız olan hasta günlük işlerini yapamayacak duruma gelmiştir. Hastanın dış merkezde yapılan tetkiklerinde Glutamik Dekarboksilaz enzim seviyesi yüksek çıkmıştır. Bu olgu sunumunda Stiff Person Sendromlu bir hastanın, Gordon’un fonksiyonel sağlık örüntüleri modelinden yararlanarak hemşirelik bakım planı sunulmuştur. Bu olguya göre; ‘’ağrı’’, ‘’uyku örüntüsünde bozulma’’, ‘’beden gereksinimden az beslenme‘’, ‘’öz bakım eksikliği’’, ‘’beden imgesinde bozulma’’, ‘’fiziksel harekette bozulma’’, ‘’fonksiyonel inkontinans’’ tanıları ele alınmış ve tanılara yönelik girişimler yapılmıştır. Sonuç olarak; bu vakayla oldukça nadir görülen Stiff Person Sendromlu bireyin sistematik ve bütüncül değerlendirilmesi ile sendroma ilişkin farkındalık oluşması ve kanıt temelli planlanan çalışmalara yol gösterici olacağı düşünülmektedir.
Supporting Institution
Çalışmamız için hiçbir kurum ya da kişiden finansal destek alınmamıştır.
References
- Kaynaklar 1. Toothaker TB, Rubin M. Paraneoplastic neurological syndromes: a review. Neurologist 2009;15(1):21-33.
- 2. Tüzün E. Nörolojik Tutulumla Seyreden Paraneoplastik Sendromlar. Klinik Gelişim Dergisi 2010;23:71-77.
- 3. McHugh JC, Murray B, Renganathan R, Connolly S, Lynch T. GAD antibody positive paraneoplastic stiff person syndrome in a patient with renal cell carcinoma. Movement Disorders: Official Journal of the Movement Disorder Society 2007;22(9):1343-1346.
- 4. Hadavi S, Noyce AJ, Leslie RD, Giovannoni G. Stiff person syndrome. Practical Neurology 2011;11(5):272-282.
- 5. Dalakas MC. Progress and stiff challenges in understanding the role of GAD-antibodies in stiff-person syndrome. Experimental Neurology 2013;(247):303-307.
- 6. Robinson P, Anderson D, Brouwers M, Feasby TE, Hume H. Evidence-based guidelines on the use of intravenous immune globulin for hematologic and neurologic conditions. Transfusion Medicine Reviews 2007;21:3-8.
- 7. Egwuonwu S, Chedebeau F. Stiff-person syndrome: a case report and review of the literature. Journal of the National Medical Association 2010;102(12):1261.
- 8. Hegyi CA. Physical therapist management of stiff person syndrome in a 24-year-old woman. Physical Therapy 2011;91(9):1403-1411.
- 9. Dalakas MC, Rakocevic G, Dambrosia JM, Alexopoulos H, McElroy B. A double‐blind, placebo‐controlled study of rituximab in patients with stiff person syndrome. Annals Of Neurology 2017;82(2):271-277.
- 10. Dalakas MC. Treatment of Stiff-Person Syndrome In: Stephen GR, Stewart AF Eds:. Therapy Of Movement Disorders: Humana, Cham, 2019:333-335.
- 11. Sexauer W, Woodford M, Pack K, Allen A, Crawford A, Rakocevic G. Dyspnea in Patients with Stiff-Person Syndrome. The American Journal of the Medical Sciences 2019;358(4):268-272.
- 12. Enç N, Can G, Özcan Ş, Tülek Z, Uysal H, Öz Alkan H. İç Hastalıkları Hemşireliği Uygulama Öğrenci Modülü. 2.baskı. İstanbul: Nobel Tıp Kitabevleri, 2015:7-40.
- 13. Herdman TH, Kamitsuru S Eds. Nursing Diagnoses, Definitions and Classification 2015-2017. Tenth edition, UK: Wiley Blackwell, 2014.
Investigation of self efficiency-sufficiency ın patient with stiff person syndrome according to Gordon's functional health patterns model-case report
Abstract
Stiff Person Syndrome; it is an autoimmune disease that progresses in the form of rigidity in the muscles, sudden myoclonic jumps, spasms and tonic activities. The complaints of the patient A.K. appeared as a contraction in the left arm, and then spread to the right arm and back. While the patient has contractions, he also has severe pain at the same time, and he has become unable to do his daily work as the severity of the contractions increases. Glutamic Decarboxylase enzyme level was found high in the patient's external examinations. In this case report, a nursing care plan was presented by taking advantage of Gordon's functional health patterns model of a patient with Stiff Person Syndrome. According to this phenomenon; '' pain '', '' sleep pattern deterioration '', '' less-than-body nutrition '', '' lack of self-care '', '' body image deterioration '', '' physical movement deterioration '', '' functional Incontinence '' diagnoses were addressed and attempts were made to diagnose them. As a result; It is thought that systematic and holistic evaluation of Stiff Person Syndrome, which is rarely seen with this case, will raise awareness about the syndrome and guide studies that are planned based on evidence.
References
- Kaynaklar 1. Toothaker TB, Rubin M. Paraneoplastic neurological syndromes: a review. Neurologist 2009;15(1):21-33.
- 2. Tüzün E. Nörolojik Tutulumla Seyreden Paraneoplastik Sendromlar. Klinik Gelişim Dergisi 2010;23:71-77.
- 3. McHugh JC, Murray B, Renganathan R, Connolly S, Lynch T. GAD antibody positive paraneoplastic stiff person syndrome in a patient with renal cell carcinoma. Movement Disorders: Official Journal of the Movement Disorder Society 2007;22(9):1343-1346.
- 4. Hadavi S, Noyce AJ, Leslie RD, Giovannoni G. Stiff person syndrome. Practical Neurology 2011;11(5):272-282.
- 5. Dalakas MC. Progress and stiff challenges in understanding the role of GAD-antibodies in stiff-person syndrome. Experimental Neurology 2013;(247):303-307.
- 6. Robinson P, Anderson D, Brouwers M, Feasby TE, Hume H. Evidence-based guidelines on the use of intravenous immune globulin for hematologic and neurologic conditions. Transfusion Medicine Reviews 2007;21:3-8.
- 7. Egwuonwu S, Chedebeau F. Stiff-person syndrome: a case report and review of the literature. Journal of the National Medical Association 2010;102(12):1261.
- 8. Hegyi CA. Physical therapist management of stiff person syndrome in a 24-year-old woman. Physical Therapy 2011;91(9):1403-1411.
- 9. Dalakas MC, Rakocevic G, Dambrosia JM, Alexopoulos H, McElroy B. A double‐blind, placebo‐controlled study of rituximab in patients with stiff person syndrome. Annals Of Neurology 2017;82(2):271-277.
- 10. Dalakas MC. Treatment of Stiff-Person Syndrome In: Stephen GR, Stewart AF Eds:. Therapy Of Movement Disorders: Humana, Cham, 2019:333-335.
- 11. Sexauer W, Woodford M, Pack K, Allen A, Crawford A, Rakocevic G. Dyspnea in Patients with Stiff-Person Syndrome. The American Journal of the Medical Sciences 2019;358(4):268-272.
- 12. Enç N, Can G, Özcan Ş, Tülek Z, Uysal H, Öz Alkan H. İç Hastalıkları Hemşireliği Uygulama Öğrenci Modülü. 2.baskı. İstanbul: Nobel Tıp Kitabevleri, 2015:7-40.
- 13. Herdman TH, Kamitsuru S Eds. Nursing Diagnoses, Definitions and Classification 2015-2017. Tenth edition, UK: Wiley Blackwell, 2014.
Details
| Primary Language | Turkish |
|---|---|
| Subjects | Health Care Administration |
| Journal Section | Articles |
| Authors | |
| Publication Date | April 30, 2021 |
| Submission Date | June 25, 2020 |
| Acceptance Date | September 22, 2020 |
| Published in Issue | Year 2021 Volume: 14 Issue: 1 |
Cite
MEU Journal of Health Sciences Assoc was began to the publishing process in 2008 under the supervision of Assoc. Prof. Gönül Aslan, Editor-in-Chief, and affiliated to Mersin University Institute of Health Sciences. In March 2015, Prof. Dr. Caferi Tayyar Şaşmaz undertook the Editor-in Chief position and since then he has been in charge.
Publishing in three issues per year (April - August - December), it is a multisectoral refereed scientific journal. In addition to research articles, scientific articles such as reviews, case reports and letters to the editor are published in the journal. Our journal, which has been published via e-mail since its inception, has been published both online and in print. Following the Participation Agreement signed with TÜBİTAK-ULAKBİM Dergi Park in April 2015, it has started to accept and evaluate online publications.
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